Paediatric Cardiac Services, Narayana Institute of Cardiac Sciences, Bengaluru, India.
Medical Student, MS Ramaiah Medical College, Bengaluru, India.
Cardiol Young. 2022 Mar;32(3):410-414. doi: 10.1017/S1047951121002298. Epub 2021 Jun 17.
Tetralogy of Fallot with pulmonary atresia is a group of congenital cardiac malformations, which is defined by the absence of luminal continuity between both ventricles and the pulmonary artery, and an interventricular communication. Pulmonary arterial supply in patients with tetralogy of Fallot with pulmonary atresia can be via the arterial duct or from collateral arteries arising directly or indirectly from the aorta (systemic-to-pulmonary artery collaterals), or rarely both. The rarest sources of pulmonary blood flow are aortopulmonary window and fistulous communication with the coronary artery.Herein, we describe an outflow tract malformation, tetralogy of Fallot with pulmonary atresia and aortopulmonary window, which was misdiagnosed as common arterial trunk. We emphasise the morphological differences.
法洛四联症合并肺动脉闭锁是一组先天性心脏畸形,其定义为左右心室与肺动脉之间无腔隙连续性,以及室间隔缺损。法洛四联症合并肺动脉闭锁患者的肺动脉血供可以通过动脉导管或直接或间接发自主动脉的侧支循环(体肺侧支循环)提供,极少数情况下两者皆有。肺血流的最罕见来源是主动脉肺动脉窗和与冠状动脉的瘘管交通。在此,我们描述了一种流出道畸形,即法洛四联症合并肺动脉闭锁和主动脉肺动脉窗,其被误诊为共同动脉干。我们强调了形态学差异。