Shimizu Kasumi, Hayashi Miho, Ito Nozomi, Hamada Kokoro, Koizumi Gaku, Kurohara Kazuto, Arai Naoya
Department of Oral and Maxillofacial Surgery, Department of Clinical Sciences, Medical Life Science, Mie University Graduate School of Medicine, Tsu, Mie 514-8507, Japan.
Case Rep Dent. 2021 Sep 20;2021:9918199. doi: 10.1155/2021/9918199. eCollection 2021.
Chédiak-Higashi syndrome (CHS), a rare autosomal recessive disorder associated with leukocyte dysfunction, is characterised by partial skin and hair albinism, immunodeficiency, and abnormal bleeding. Furthermore, it may be associated with cognitive and neurological impairments. The long-term prognosis of patients is generally poor, and haematopoietic stem cell transplantation is a radical immunodeficiency treatment. Here, we report a case of successful oral management of an 18-year-old woman with CHS accompanied by aggressive periodontitis who underwent haematopoietic stem cell transplantation.
切-东综合征(CHS)是一种与白细胞功能障碍相关的罕见常染色体隐性疾病,其特征为部分皮肤和毛发白化、免疫缺陷及异常出血。此外,它可能与认知和神经功能障碍有关。患者的长期预后通常较差,造血干细胞移植是一种根治性免疫缺陷治疗方法。在此,我们报告一例成功通过口腔治疗一名18岁患有CHS并伴有侵袭性牙周炎的女性患者,该患者接受了造血干细胞移植。