Department of Pediatric Radiology, Regina Margherita Children's Hospital, Turin, Italy.
Department of Radiology and Clinical Physiology, Queen Silvia Children's Hospital, Sahlgrenska University Hospital, Göteborg, Sweden.
Pediatr Radiol. 2021 Dec;51(13):2598-2606. doi: 10.1007/s00247-021-05173-x. Epub 2021 Oct 15.
Since Francis Fontan first introduced the eponymous technique, the Fontan procedure, this type of surgical palliation has allowed thousands of children affected by specific heart malformations to reach adulthood. Nevertheless, abdominal, thoracic, lymphatic and neurologic complications are the price that is paid by these patients. Our review focuses on Fontan-associated liver disease; the purpose is to summarize the current understanding of its physiopathology, the aim of follow-up and the specific radiologic follow-up performed in Europe. Finally, we as members of the Abdominal Task Force of the European Society of Paediatric Radiology propose a consensus-based imaging follow-up algorithm.
自弗朗西斯·方丹（Francis Fontan）首次引入同名技术——方丹手术以来，这种手术姑息疗法已经使数千名患有特定心脏畸形的儿童能够成年。然而，腹部、胸部、淋巴和神经系统并发症是这些患者必须付出的代价。我们的综述重点关注方丹相关的肝病；目的是总结其病理生理学的当前认识、随访的目标以及在欧洲进行的特定放射学随访。最后，作为欧洲儿科放射学会腹部工作组的成员，我们提出了一个基于共识的影像学随访算法。
