患有眼咽型肌营养不良症的咽鼓管异常开放患者。
Patulous Eustachian Tube Patients With Oculopharyngeal Muscular Dystrophy.
作者信息
Ishigakii Kento, Ikeda Ryoukichi, Suzuki Jun, Hirano-Kawamoto Ai, Ohta Jun, Kato Kengo, Izumi Rumiko, Suzuki Naoki, Aoki Masashi, Kawase Tetsuaki, Katori Yukio
机构信息
Department of Otolaryngology-Head and Neck Surgery, Tohoku University School of Medicine, Sendai.
Sen-En Rifu Otological Surgery Center, Miyagi.
出版信息
Otol Neurotol. 2022 Apr 1;43(4):e442-e445. doi: 10.1097/MAO.0000000000003494.
OBJECTIVES
To describe cases of patulous Eustachian tube (PET) or patent ET conditions in oculopharyngeal muscular dystrophy (OPMD).
PATIENTS
Four cases of PET or patent ET conditions with OPMD.
MAIN OUTCOME MEASURES
Clinical case records, objective ET function tests (tubo-tympano-aerodynamic graphy and sonotubometry), and swallowing function (videoendoscopic examination and Food Intake Level Scale) were analyzed.
RESULTS
Two cases of definite PET, one case of possible PET, and one case lacking aural symptoms with findings of patent ET. All patients have ptosis, and three cases have dysphagia. Body mass index indicated that three cases were underweight. Magnetic resonance imaging in case 4 showed atrophy and fat replacement of palatine and masticatory muscles.
CONCLUSIONS
It is important to consider PET or patent ET conditions when OPMD patients describe aural symptoms.
目的
描述眼咽型肌营养不良症（OPMD）中咽鼓管异常开放（PET）或咽鼓管通畅的病例情况。
患者
4例患有OPMD且伴有PET或咽鼓管通畅情况的病例。
主要观察指标
分析临床病例记录、客观的咽鼓管功能测试（鼓室-咽鼓管空气动力学造影和咽鼓管测声法）以及吞咽功能（视频内镜检查和食物摄入水平量表）。
结果
2例确诊为PET，1例可能为PET，1例无耳部症状但检查发现咽鼓管通畅。所有患者均有上睑下垂，3例有吞咽困难。身体质量指数显示3例体重过轻。病例4的磁共振成像显示腭肌和咀嚼肌萎缩及脂肪替代。
结论
当OPMD患者描述耳部症状时，考虑PET或咽鼓管通畅情况很重要。
Zotero 插件