Department of Orthopedic, King Saud University, Riyadh, Saudi Arabia.
Department of Orthopedics, King Saud University, Riyadh, Saudi Arabia.
Am J Case Rep. 2022 Oct 4;23:e936627. doi: 10.12659/AJCR.936627.
BACKGROUND Arthrogryposis is a congenital condition of multiple contractures of joints associated with hip dislocation. The outcome of open reduction of hip dislocation in arthrogryposis patients is debatable. Open reduction of arthrogryposis is challenging for shallow acetabulum and extensive adhesions and fibrosis. For this reason, a careful extensive release must be carried out to achieve the open reduction of the hip in arthrogryposis patients. The literature lacks surgical recommendations for open reduction of the hip in arthrogryposis patients and how to deal with cases of the extruded bone segment during open reduction. CASE REPORT The patient presented in the first few weeks of life with bilateral clubfoot and left hip dislocation. Clinical diagnosis of arthrogryposis was made after referral to a genetics specialist. The hip was clinically irreducible. The patient underwent open reduction and femoral shortening using the Smith Peterson approach at the age of 15 months, with accidental extrusion of the proximal femur, which was retained immediately. The clinical outcome showed a painless, good range of motion. Radiographically, features of avascular necrosis and healed osteotomy site were evident. CONCLUSIONS A difficult hip reduction was expected in this arthrogryposis patient, which required careful dissection of surrounding fibrosis and appropriate femoral shortening. Careful dissection should be carried out during open reduction to avoid jeopardization of femoral head vascularity or even complete devitalization of the proximal femur.
先天性多关节挛缩症伴髋关节脱位,其髋关节脱位的切开复位效果存在争议。先天性多关节挛缩症患者的髋臼较浅且存在广泛的粘连和纤维化,因此为实现髋关节的切开复位,必须进行仔细的广泛松解。文献中缺乏先天性多关节挛缩症患者髋关节切开复位的手术建议,也缺乏如何处理切开复位过程中骨块脱出的情况。
患者在出生后的数周内出现双侧马蹄内翻足和左侧髋关节脱位。转至遗传专家后,临床诊断为先天性多关节挛缩症。髋关节触诊时无法复位。患儿在 15 月龄时接受了 Smith-Peterson 入路切开复位和股骨短缩术,术中意外发生股骨近端脱出,立即予以保留。临床结果显示无痛、关节活动度良好。影像学检查显示存在股骨头缺血性坏死和愈合的截骨部位。
该先天性多关节挛缩症患者髋关节复位困难,需要仔细分离周围纤维化组织并适当进行股骨短缩。切开复位时应仔细操作,以避免股骨头血供受损,甚至股骨近端完全失活。