Kahraman Nail, Topal Dursun, Coşkun Gültekin, Tiryakioğlu Selma Kenar, Topal Serra, Güler Sena, Binicier Nöfel Ahmet, Koca Fatih, Demir Deniz
Department of Cardiovasculary Surgery, University of Health Sciences, Bursa City Hospital, Bursa, Turkey.
Department of Cardiology, University of Health Sciences, Bursa City Hospital, Bursa, Turkey.
Echocardiography. 2023 Apr;40(4):359-363. doi: 10.1111/echo.15547. Epub 2023 Mar 7.
Among masses involving the mitral valve and annulus, caseous calcification of the mitral annulus (CCMA) is a rare disease. CCMA accounts for .63% of all mitral annular calcification (MAC) cases. The pathophysiology is still unknown. The correct diagnosis and treatment of this disease is very important to prevent complications. We present a case of giant CCMA with advanced mitral stenosis and hypertrophic cardiomyopathy, presenting with symptoms of infection and therefore a preliminary diagnosis of infective endocarditis. Because of these features, we wanted to share our case as it is the 1st case in the literature.
在累及二尖瓣和瓣环的病变中,二尖瓣瓣环干酪样钙化(CCMA)是一种罕见疾病。CCMA占所有二尖瓣环钙化(MAC)病例的0.63%。其病理生理学仍不清楚。正确诊断和治疗这种疾病对于预防并发症非常重要。我们报告一例巨大CCMA合并晚期二尖瓣狭窄和肥厚型心肌病的病例,该病例表现为感染症状,因此初步诊断为感染性心内膜炎。鉴于这些特征,我们想分享我们的病例,因为这是文献中的首例。