Cicek Murat, Onalan Mehmet Akif, Ilker Yucel, Ozkok Sercin, Ozdemir Fatih, Yurdakok Okan, Aydemir Numan Ali, Sasmazel Ahmet
Department of Pediatric Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey.
Department of Pediatric Cardiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey.
Cardiol Young. 2023 Sep;33(9):1700-1705. doi: 10.1017/S1047951123000860. Epub 2023 Apr 13.
Anomalous aortic origin of the coronary artery is a rare congenital cardiac anomaly. The aim of this study was to present our experience with patients who underwent surgery for the anomalous aortic origin of the coronary artery.
This was a retrospective review of our experience with patients who had anomalous aortic origin of the coronary artery from 2019 to 2022.
Seven patients were managed for anomalous aortic origin of the coronary artery, including five males and two females. The median age of the patients were 16 years (IQR, 14.5-26 years). Five patients had anomalous aortic origin of the right coronary artery and two patients had anomalous aortic origin of the left coronary artery. Five patients were treated surgically, one patient refused surgical treatment despite myocardial ischaemia symptoms, and the other one was not operated because she had no symptoms. Two patients underwent pulmonary root anterior translocation and left main coronary artery unroofing procedure, one patient underwent right coronary artery unroofing procedure, one patient underwent pulmonary artery lateral translocation procedure, and the last patient underwent right coronary artery osteal translocation procedure. The post-operative mortality or myocardial infarction was not observed in any patient. Patients were followed for a median of 10 months (IQR, 6.75-20.5 months) after repair.
The data suggest that surgical repair of anomalous aortic origin of the coronary artery can be performed confidently and can be very effective for relieving myocardial ischaemia symptoms. Different surgical techniques can be used in anomalous aortic origin of the coronary artery according to the course and origin of the coronary arteries. To the our knowledge, pulmonary root anterior translocation and coronary artery unroofing procedure were performed for the first time in the literature.
冠状动脉异常起源于主动脉是一种罕见的先天性心脏异常。本研究的目的是介绍我们对接受冠状动脉异常起源于主动脉手术患者的经验。
这是对我们2019年至2022年期间冠状动脉异常起源于主动脉患者经验的回顾性研究。
7例患者接受了冠状动脉异常起源于主动脉的治疗,其中男性5例,女性2例。患者的中位年龄为16岁(四分位间距,14.5 - 26岁)。5例患者右冠状动脉异常起源于主动脉,2例患者左冠状动脉异常起源于主动脉。5例患者接受了手术治疗,1例患者尽管有心肌缺血症状但拒绝手术治疗,另1例患者因无症状未接受手术。2例患者接受了肺动脉根部前移位和左主冠状动脉开窗术,1例患者接受了右冠状动脉开窗术,1例患者接受了肺动脉侧移位术,最后1例患者接受了右冠状动脉骨段移位术。所有患者均未观察到术后死亡或心肌梗死。修复术后患者的中位随访时间为10个月(四分位间距,6.75 - 20.5个月)。
数据表明,冠状动脉异常起源于主动脉的手术修复可以放心进行,并且对于缓解心肌缺血症状非常有效。根据冠状动脉的走行和起源,可在冠状动脉异常起源于主动脉时采用不同的手术技术。据我们所知,肺动脉根部前移位和冠状动脉开窗术在文献中首次进行。