Calò Leonardo, Oliviero Giada, Crescenzi Cinzia, Romeo Fabiana, Martino Annamaria, Bressi Edoardo, Stefanini Matteo, Silvetti Elisa, Danza Ludovica, Rebecchi Marco, Canestrelli Stefano, Fedele Elisa, Lanzillo Chiara, Fusco Armando, De Ruvo Ermenegildo
Division of Cardiology, Policlinico Casilino, Via Casilina 1049, 00169 Rome, Italy.
Division of Radiology, Policlinico Casilino, Via Casilina 1049, 00169 Rome, Italy.
Eur Heart J Suppl. 2023 Apr 26;25(Suppl C):C169-C172. doi: 10.1093/eurheartjsupp/suad019. eCollection 2023 May.
Criteria for diagnosis of arrhythmogenic cardiomyopathy (ACM) were first proposed in 1994 and subsequently revised in 2010 and in 2020 by an international task force. According to the last consensus of 2020, ACM is defined as a heart muscle disease affecting right ventricle, left ventricle or both, whose principal pathologic feature is fibrofatty myocardial replacement that impairs systolic ventricular function and predisposes to lethal ventricular arrhythmias. ECG findings not only could help to early recognize affected patients but also could identify the ones with maximum risk of ventricular arrhythmias and sudden cardiac death.
致心律失常性心肌病(ACM)的诊断标准最早于1994年提出,随后在2010年和2020年由一个国际特别工作组进行了修订。根据2020年的最新共识,ACM被定义为一种影响右心室、左心室或两者的心肌疾病,其主要病理特征是纤维脂肪性心肌替代,这会损害心室收缩功能并易引发致命性室性心律失常。心电图检查结果不仅有助于早期识别受影响的患者,还能识别出室性心律失常和心源性猝死风险最高的患者。