Yadav Pramodman Singh, Shah Leeza, Rayamajhi Anusha, Mehta Binod, Bhurtel Min Raj, Adhikari Pratik, Shrestha Manisha, Bhattarai Sashank
B.P. Koirala Institute of Health Sciences Dharan Nepal.
Department of Internal Medicine Chitwan Medical College and Teaching Hospital Chitwan Nepal.
Clin Case Rep. 2024 Jan 2;12(1):e8392. doi: 10.1002/ccr3.8392. eCollection 2024 Jan.
Unilateral opercular lesions can result in Foix-Chavany-Marie syndrome, which is marked by acute anarthria, automatic-voluntary movement dissociation-most notably the absence of voluntary facial and tongue movements-and a generally better prognosis. Better patient outcomes are mostly dependent on early detection, management, and rehabilitation.
Opercular syndrome is a rare neurological disorder caused by bilateral or unilateral lesions of the operculum that result in symptoms related to speech and swallowing difficulties with dissociation of automatic-voluntary movements in affected muscles. 78-year-old female presented with acute onset dysarthria, left sided facial deviation and difficulties in chewing, speaking, and swallowing. CT head revealed ischemic changes in left frontal operculum and was diagnosed with the unilateral opercular syndrome. The case was managed according to ischemic stroke protocol. The patient was discharged after 7 days of hospital stay, with MRS 2, NIHSS 9 and secondary stroke preventive measures. At 4 months follow-up, her MRS was 1, with mild dysarthria, that could be understood, and her swallowing improved to some amount of drooling while feeding. Early recognition, treatment, and rehabilitation play important role in prompt improvement of symptoms.
单侧岛盖部病变可导致福-恰-马综合征,其特征为急性构音障碍、自主运动与随意运动分离(最显著的是缺乏面部和舌的随意运动),且预后通常较好。更好的患者预后大多取决于早期检测、管理和康复。
岛盖综合征是一种罕见的神经系统疾病,由岛盖部的双侧或单侧病变引起,导致与言语和吞咽困难相关的症状,以及受累肌肉的自主运动与随意运动分离。一名78岁女性出现急性构音障碍、左侧面部偏斜以及咀嚼、说话和吞咽困难。头颅CT显示左侧额岛盖部有缺血性改变,被诊断为单侧岛盖综合征。该病例按照缺血性卒中方案进行管理。患者住院7天后出院,改良Rankin量表评分为2分,美国国立卫生研究院卒中量表评分为9分,并采取了二级卒中预防措施。在4个月的随访中,她的改良Rankin量表评分为1分,有轻度构音障碍但可理解,吞咽功能有所改善,进食时仅有少量流涎。早期识别、治疗和康复对症状的迅速改善起着重要作用。