Chen Irene Y, Dunne Richard F, Liao Xiaoyan
Department of Pathology and Laboratory Medicine, University of Rochester Medical Center, Rochester, NY, USA.
Department of Medicine, Wilmot Cancer Institute, University of Rochester Medical Center, Rochester, NY, USA.
Virchows Arch. 2025 Feb;486(2):323-332. doi: 10.1007/s00428-024-03787-8. Epub 2024 Mar 19.
Intrahepatic cholangiocarcinoma (ICC) is a highly aggressive malignant neoplasm. Certain histologic features and the tumor microenvironment may impact disease progression. We aim to characterize the clinicopathologic features of ICC to identify prognostic factors. A total of 50 surgically resected ICC (partial or transplant) cases were analyzed. The cohort included 26 men and 24 women with a median age of 62 years. Eighteen (36%) cases were multifocal ICC with a mean largest tumor size of 6.5 cm. Neoadjuvant and adjuvant chemotherapy was done in eight (16%) and 33 (66%) patients, respectively. Histologically, 42 (84%) were small duct type, seven (14%) large duct type, and one mixed (2%). Thirty (60%) cases showed lymphovascular invasion (LVI) and 11 (22%) with perineural invasion (PNI). Twenty-eight (56%) cases demonstrated dense intratumoral hyaline fibrosis and 18 (36%) with tumor necrosis, each ≥ 10% tumor volume. On follow-up, 35 (70%) patients died of disease after a median disease-specific survival (DSS) of 21 months. Univariate analysis revealed that hyaline fibrosis and adjuvant chemotherapy were associated with better DSS, while tumor size, multifocality, necrosis, and peritumoral neutrophil to lymphocyte ratio were associated with worse DSS. In contrast, age, sex, small vs. large duct types, LVI, and individual inflammatory cell counts were not significant prognostic factors. In summary, ICC is a heterogeneous malignancy with variable clinical courses associated with tumor burden, histology, and microenvironment. Targeting specific components within the tumor microenvironments may be a promising approach for treatment in the future.
肝内胆管癌(ICC)是一种侵袭性很强的恶性肿瘤。某些组织学特征和肿瘤微环境可能会影响疾病进展。我们旨在描述ICC的临床病理特征以确定预后因素。共分析了50例手术切除的ICC(部分切除或移植)病例。该队列包括26名男性和24名女性,中位年龄为62岁。18例(36%)为多灶性ICC,平均最大肿瘤大小为6.5厘米。分别有8例(16%)和33例(66%)患者接受了新辅助化疗和辅助化疗。组织学上,42例(84%)为小胆管型,7例(14%)为大胆管型,1例为混合型(2%)。30例(60%)病例显示有淋巴管侵犯(LVI),11例(22%)有神经周围侵犯(PNI)。28例(56%)病例显示肿瘤内有致密的透明样纤维化,18例(36%)有肿瘤坏死,两者均占肿瘤体积的≥10%。随访时,35例(70%)患者在疾病特异性生存(DSS)中位数为21个月后死于疾病。单因素分析显示,透明样纤维化和辅助化疗与较好的DSS相关,而肿瘤大小、多灶性、坏死和肿瘤周围中性粒细胞与淋巴细胞比值与较差的DSS相关。相比之下,年龄、性别、小胆管型与大胆管型、LVI以及单个炎症细胞计数不是显著的预后因素。总之,ICC是一种异质性恶性肿瘤,其临床病程多变,与肿瘤负荷、组织学和微环境有关。针对肿瘤微环境中的特定成分可能是未来一种有前景的治疗方法。