Department of Molecular and Cellular Neurobiology, Center for Neurogenomics and Cognitive Research, Vrije Universiteit Amsterdam, Amsterdam, The Netherlands.
Department of Clinical Pharmacy and Pharmacology, University Medical Center Groningen, Groningen, The Netherlands.
Acta Neuropathol Commun. 2024 Jun 4;12(1):86. doi: 10.1186/s40478-024-01800-4.
Tau protein hyperphosphorylation and aggregation are key pathological events in neurodegenerative tauopathies such as Alzheimer's disease. Interestingly, seasonal hibernators show extensive tau hyperphosphorylation during torpor, i.e., the hypothermic and hypometabolic state of hibernation, which is completely reversed during arousal. Torpor-associated mechanisms that reverse tau hyperphosphorylation may be of therapeutic relevance, however, it is currently not known to what extent they apply to human tau. Here we addressed this issue using daily torpor in wildtype mice that express mouse tau (mtau) and in mice that lack mtau expression and instead express human tau (htau). AT8, AT100 and Ser396 immunoblotting and immunohistochemistry were used to assess tau (hyper)phosphorylation at clinically relevant phosphorylation sites. We found that torpor robustly and reversibly increases the levels of phosphorylated tau in both mtau and htau mice. Immunohistochemistry revealed four brain areas that show prominent tau phosphorylation: the hippocampus, posterior parietal cortex, piriform cortex and cortical amygdala. Whereas wildtype mice primarily showed increased levels of diffusely organized hyperphosphorylated tau during torpor, htau mice contained clear somato-dendritic accumulations of AT8 reactivity resembling tau pre-tangles as observed in the Alzheimer brain. Interestingly, AT8-positive accumulations disappeared upon arousal, and tau phosphorylation levels at 24 h after arousal were lower than observed at baseline, suggesting a beneficial effect of torpor-arousal cycles on preexisting hyperphosphorylated tau. In conclusion, daily torpor in mice offers a quick and standardized method to study tau phosphorylation, accumulation and clearance in mouse models relevant for neurodegeneration, as well as opportunities to discover new targets for the treatment of human tauopathies.
tau 蛋白过度磷酸化和聚集是神经退行性 tau 病(如阿尔茨海默病)的关键病理事件。有趣的是,季节性冬眠动物在蛰伏(即冬眠的低温和低代谢状态)期间表现出广泛的 tau 过度磷酸化,这种过度磷酸化在苏醒时完全逆转。与蛰伏相关的逆转 tau 过度磷酸化的机制可能具有治疗相关性,然而,目前尚不清楚它们在多大程度上适用于人类 tau。在这里,我们使用野生型小鼠的每日蛰伏来解决这个问题,这些小鼠表达小鼠 tau(mtau)和缺乏 mtau 表达但表达人类 tau(htau)的小鼠。使用 AT8、AT100 和 Ser396 免疫印迹和免疫组织化学来评估与临床相关磷酸化位点的 tau(过度)磷酸化。我们发现,蛰伏强烈且可逆地增加了 mtau 和 htau 小鼠中磷酸化 tau 的水平。免疫组织化学显示出四个大脑区域显示出明显的 tau 磷酸化:海马体、后顶叶皮层、梨状皮层和皮质杏仁核。虽然野生型小鼠在蛰伏期间主要表现出弥漫性组织 tau 过度磷酸化水平增加,但 htau 小鼠含有清晰的 somato-dendritic AT8 反应性聚集物,类似于阿尔茨海默病大脑中观察到的 tau 前缠结。有趣的是,AT8 阳性聚集物在苏醒后消失,并且苏醒后 24 小时的 tau 磷酸化水平低于基线时的水平,这表明蛰伏-苏醒周期对先前存在的过度磷酸化 tau 具有有益作用。总之,小鼠的每日蛰伏为研究与神经退行性变相关的小鼠模型中的 tau 磷酸化、积累和清除提供了一种快速和标准化的方法,也为发现治疗人类 tau 病的新靶点提供了机会。