Internal Medicine, Allegheny Health Network, Pittsburgh, Pennsylvania, USA
Allegheny Health Network, Pittsburgh, Pennsylvania, USA.
BMJ Case Rep. 2024 Jun 25;17(6):e259863. doi: 10.1136/bcr-2024-259863.
Scleromalacia perforans, or necrotising anterior scleritis, is a rare and severe form of eye disease that usually occurs in patients suffering from long-standing systemic inflammatory diseases, with rheumatoid arthritis (RA) being the most common. Here, we report the case of a patient who presented with redness of the eye and discolouration of the sclera and was diagnosed with scleromalacia perforans without any further extraophthalmic systemic involvement. Serological workup revealed highly positive cyclic citrullinated peptide (CCP) antibody (CCP-IgG/anticitrullinated protein antibodies) and positive rheumatoid factor, serologies commonly associated with RA. The patient's symptoms responded very well to rituximab therapy.
穿孔性巩膜软化症,又称坏死性前部巩膜炎,是一种罕见且严重的眼部疾病,通常发生于患有长期系统性炎症性疾病的患者中,其中类风湿关节炎(RA)最为常见。在此,我们报告了一例以眼部发红和巩膜变色为表现、并诊断为穿孔性巩膜软化症而无任何其他眼外全身受累的患者。血清学检查显示高滴度的环瓜氨酸肽(CCP)抗体(CCP-IgG/抗瓜氨酸蛋白抗体)和阳性类风湿因子,这些血清学标志物通常与 RA 相关。该患者的症状对利妥昔单抗治疗反应非常好。