低体重合并主动脉弓中断和主动脉闭锁患者的双心室修复术。
Biventricular repair in low-weight patient with interrupted aortic arch and aortic atresia.
作者信息
Soynov Ilya A, Arkhipov Alexey N, Manukian Serezha N, Kulyabin Yuriy Y, Kobelev Evgeniy, Malakhova Oksana Y, Voitov Alexey V, Suzdalova Olga A
机构信息
Department of Pediatric Cardiac Surgery, E. Meshalkin National Medical Research Center, Ministry of Health of Russian Federation, Rechkunovskaya Str. 15, Novosibirsk, Russia, 630055.
出版信息
Egypt Heart J. 2024 Jul 4;76(1):84. doi: 10.1186/s43044-024-00516-z.
BACKGROUND
Aortic atresia with ventricular septal defect is a very rare congenital cardiac anomaly, especially in combination with aortic arch interruption. It is always challenging to choose the optimal treatment tactics for such patients. One of the possible types of intervention is the Yasui procedure. There are only 19 reported cases in the literature of aortic atresia with interruption of the aortic arch type B or C, and not a single clinical case of type A.
CASE PRESENTATION
The proband was a 2-day-old boy with diagnosis: aortic atresia with a ventricular septal defect and interruption of the aortic arch type B. The child underwent a Yasui procedure without serious postoperative complications and with good long-term result.
CONCLUSIONS
The Yasui procedure in patients with aortic atresia and interrupted aortic arch can be performed with minimal complications, even in low-weight patients.
背景
主动脉闭锁合并室间隔缺损是一种非常罕见的先天性心脏畸形，尤其是合并主动脉弓中断时。为这类患者选择最佳治疗策略始终具有挑战性。一种可能的干预类型是安井手术。文献中仅报道了19例B型或C型主动脉弓中断的主动脉闭锁病例，尚无A型的临床病例。
病例报告
先证者是一名2日龄男婴，诊断为：主动脉闭锁合并室间隔缺损及B型主动脉弓中断。该患儿接受了安井手术，术后无严重并发症，长期效果良好。
结论
即使是低体重患者，主动脉闭锁合并主动脉弓中断患者行安井手术时并发症也可降至最低。
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