Institute for Fundamental Biomedical Research, Biomedical Sciences Research Center (BSRC) "Alexander Fleming", Vari, Greece.
School of Biology, Aristotle University of Thessaloniki, Thessaloniki, Macedonia, Greece.
Cell Death Dis. 2024 Aug 9;15(8):584. doi: 10.1038/s41419-024-06966-2.
TNF is a potent cytokine known for its involvement in physiology and pathology. In Rheumatoid Arthritis (RA), persistent TNF signals cause aberrant activation of synovial fibroblasts (SFs), the resident cells crucially involved in the inflammatory and destructive responses of the affected synovial membrane. However, the molecular switches that control the pathogenic activation of SFs remain poorly defined. Cyld is a major component of deubiquitination (DUB) machinery regulating the signaling responses towards survival/inflammation and programmed necrosis that induced by cytokines, growth factors and microbial products. Herein, we follow functional genetic approaches to understand how Cyld affects arthritogenic TNF signaling in SFs. We demonstrate that in spontaneous and induced RA models, SF-Cyld DUB deficiency deteriorates arthritic phenotypes due to increased levels of chemokines, adhesion receptors and bone-degrading enzymes generated by mutant SFs. Mechanistically, Cyld serves to restrict the TNF-induced hyperactivation of SFs by limiting Tak1-mediated signaling, and, therefore, leading to supervised NF-κB and JNK activity. However, Cyld is not critically involved in the regulation of TNF-induced death of SFs. Our results identify SF-Cyld as a regulator of TNF-mediated arthritis and inform the signaling landscape underpinning the SF responses.
肿瘤坏死因子(TNF)是一种具有生理和病理作用的强效细胞因子。在类风湿关节炎(RA)中,持续的 TNF 信号会导致滑膜成纤维细胞(SFs)异常激活,SFs 是参与受影响滑膜炎症和破坏反应的重要固有细胞。然而,控制 SF 致病激活的分子开关仍未得到很好的定义。Cyld 是调节细胞因子、生长因子和微生物产物诱导的存活/炎症和程序性坏死信号反应的去泛素化(DUB)机制的主要组成部分。在此,我们采用功能遗传方法来了解 Cyld 如何影响 SF 中的致关节炎 TNF 信号。我们证明,在自发性和诱导性 RA 模型中,SF-Cyld DUB 缺陷由于突变 SF 产生的趋化因子、粘附受体和骨降解酶水平升高,导致关节炎表型恶化。从机制上讲,Cyld 通过限制 Tak1 介导的信号转导来限制 TNF 诱导的 SF 过度激活,从而导致受监督的 NF-κB 和 JNK 活性。然而,Cyld 并不参与调节 TNF 诱导的 SF 死亡。我们的结果将 SF-Cyld 确定为 TNF 介导的关节炎的调节剂,并为 SF 反应的信号转导景观提供信息。