Yaynishet Yodit Abraham, Kibrom Bethlehem Tesfasilassie, Abera Michael Teklehaimanot, Legesse Tesfaye Kebede
Department of Radiology, College of Health Sciences, Addis Ababa University, Addis Ababa, Ethiopia.
Centre for Innovative Drug Development and Therapeutic Trials for Africa (CDT-Africa), College of Health Sciences, Addis Ababa University, Addis Ababa, Ethiopia.
Radiol Case Rep. 2024 Oct 9;20(1):97-100. doi: 10.1016/j.radcr.2024.09.137. eCollection 2025 Jan.
Vascular ring anomalies, represented mainly by the double aortic arch (DAA), account for about 1% of congenital cardiovascular anomalies and are characterized by tracheoesophageal compression due to encircling vascular or ligamentous structures. These anomalies arise from the failure of the right fourth aortic arch to regress during embryonic development, leading to symptoms ranging from respiratory distress to dysphagia. Diagnostic imaging includes chest radiography, CT, MRI, and echocardiography, each with specific considerations, especially in pediatric patients. Management, often surgical, focuses on relieving compression symptoms and has a favorable prognosis. This case series emphasizes the manifestations of the double aortic arch, whether it be respiratory distress or dysphagia, and addresses both right and left dominant arches.
血管环异常主要以双主动脉弓(DAA)为代表,约占先天性心血管异常的1%,其特征是由于环绕的血管或韧带结构导致气管食管受压。这些异常是由于胚胎发育过程中右第四主动脉弓未能退化所致,可导致从呼吸窘迫到吞咽困难等一系列症状。诊断性影像学检查包括胸部X线摄影、CT、MRI和超声心动图,每种检查都有特定的注意事项,尤其是在儿科患者中。治疗通常采用手术,重点是缓解压迫症状,预后良好。本病例系列强调了双主动脉弓的表现,无论是呼吸窘迫还是吞咽困难,并涉及右优势弓和左优势弓。