Martín David Gómez, Sánchez-Rubio Lezcano Juan, Fuertes Ferre Georgina, Álvarez Roy Laura, López Ramón Marta, Diarte De Miguel José Antonio
Cardiology Service, Miguel Servet University Hospital, Zaragoza, Spain.
Interventional Cardiology Unit, Miguel Servet University Hospital, Zaragoza, Spain.
Acta Cardiol. 2024 Dec;79(10):1161-1163. doi: 10.1080/00015385.2024.2434297. Epub 2024 Nov 28.
Cor Triatriatum Dexter (CTD) is a rare congenital heart malformation, with an estimated incidence of 0.025%, characterised by a membrane dividing the right atrium (RA) into two chambers. A variant, incomplete CTD (CTDi), occurs when the right membrane extends partially into the interatrial septum without fully dividing the RA. CTDi can be associated with interatrial septal defects, found in 5% of patients with atrial septal defects or a patent foramen ovale (PFO). The study reports three adult patients (46-53 years old) with CTDi and a PFO, all presenting cryptogenic stroke and referred for PFO closure. Two cases underwent percutaneous closure with guidance from fluoroscopy and 2D/3D transesophageal echocardiography (TEE), and the last one utilised intracardiac echocardiography (ICE) for device placement. In patients referred for PFO closure, CTDi is common and can complicate visualisation, prolong procedure times, and reduce success rates. Difficulties in device deployment and the risk of residual shunt or embolisation have been reported. The authors highlight that using oversizing techniques, traction manoeuvres during device deployment, and preoperative planning with advanced imaging (such as ICE or 3D TEE) are crucial for successful percutaneous closure in cases with CTDi and PFO.
右三房心(CTD)是一种罕见的先天性心脏畸形,估计发病率为0.025%,其特征是有一层膜将右心房(RA)分为两个腔室。一种变异型,不完全性CTD(CTDi),是指右房膜部分延伸至房间隔而未完全分隔右心房时出现的情况。CTDi可能与房间隔缺损有关,在5%的房间隔缺损或卵圆孔未闭(PFO)患者中可发现。该研究报告了3例成年患者(46 - 53岁)患有CTDi和PFO,均表现为不明原因的卒中并因PFO封堵而转诊。2例在荧光透视和二维/三维经食管超声心动图(TEE)引导下进行了经皮封堵,最后1例使用心腔内超声心动图(ICE)进行器械置入。在因PFO封堵而转诊的患者中,CTDi很常见,会使可视化变得复杂,延长手术时间并降低成功率。已有报道称存在器械置入困难以及残余分流或栓塞的风险。作者强调,在CTDi合并PFO的病例中,使用加大尺寸技术、器械置入过程中的牵引操作以及术前采用先进成像技术(如ICE或三维TEE)进行规划对于成功的经皮封堵至关重要。