He Dingxian, Zhong Huahua, Jin Lei, Chen Ran, Wu Zongtai, Zhao Rui, Huan Xiao, Yan Chong, Song Jie, Xi Jianying, Zhao Chongbo, Zhu Shanfeng, Luo Sushan
Huashan Rare Disease Centre and Department of Neurology, Huashan Hospital, Shanghai Medical College, National Centre for Neurological Disorders, Fudan University, Shanghai, China.
Department of Public Health and Primary Care, University of Cambridge, Cambridge, United Kingdom.
Front Immunol. 2025 May 8;16:1578359. doi: 10.3389/fimmu.2025.1578359. eCollection 2025.
To identify new metabolic biomarkers associated with myasthenia gravis (MG).
We analyzed 285 potential metabolic molecules from UK Biobank (UKB) for MG patients and identified elevated serum cystatin C (Cys-C). Validation was performed using laboratory data, ELISA, and clinical information from Chinese (CHN) acetylcholine receptor antibody (AChR-Ab) positive generalized MG (gMG) cohorts. We assessed cytokines/chemokines/complements and peripheral blood T lymphocytes using Luminex assays and flow cytometry. MG-relevant scores including myasthenia gravis activities of daily living score (MG-ADL) and quantitative myasthenia gravis score (QMG) were prospectively collected and retrospectively analyzed. The correlations between serum Cys-C and the ratio of T helper 1 (Th1)/Th2 were assessed.
Serum Cys-C levels were significantly elevated in MG patients compared to healthy controls in both UKB cohorts and Chinese MG cohorts (CHN) (UKB: 0.99 ± 0.20 vs. 0.86 ± 0.12 mg/L, p = 2.26E-41; CHN: 1.08 ± 0.30 vs. 0.87 ± 0.13 mg/L, p = 4.83E-08). Higher serum Cys-C levels were found in MG patients with high disease burden, as stratified by MG-ADL score. Serum Cys-C correlated with MG scores, including QMG (R = 0.40, p = 3.90E-03) and MG-ADL scores (R = 0.42, p = 2.40E-03). The ratio of Th1/Th2 correlated well with the serum Cys-C (R = 0.29, p = 3.10E-02).
Serum Cys-C levels were significantly elevated in AChR-Ab positive gMG patients and correlated with disease severity and Th1/Th2 ratio, suggesting its potential as an efficient biomarker for predicting the clinical severity of MG. Future prospective cohort studies with a large sample size are expected to validate these findings.
鉴定与重症肌无力(MG)相关的新代谢生物标志物。
我们分析了英国生物银行(UKB)中285种潜在的代谢分子,针对MG患者并确定血清胱抑素C(Cys-C)升高。使用实验室数据、酶联免疫吸附测定(ELISA)以及来自中国(CHN)乙酰胆碱受体抗体(AChR-Ab)阳性全身型MG(gMG)队列的临床信息进行验证。我们使用Luminex检测法和流式细胞术评估细胞因子/趋化因子/补体以及外周血T淋巴细胞。前瞻性收集并回顾性分析了包括重症肌无力日常生活活动评分(MG-ADL)和重症肌无力定量评分(QMG)在内的MG相关评分。评估血清Cys-C与辅助性T细胞1(Th1)/辅助性T细胞2(Th2)比值之间的相关性。
在UKB队列和中国MG队列(CHN)中,MG患者的血清Cys-C水平均显著高于健康对照(UKB:0.99±0.20 vs. 0.86±0.12mg/L,p = 2.26E-41;CHN:1.08±0.30 vs. 0.87±0.13mg/L,p = 4.83E-08)。根据MG-ADL评分分层,疾病负担高的MG患者血清Cys-C水平更高。血清Cys-C与MG评分相关,包括QMG(R = 0.40,p = 3.90E-03)和MG-ADL评分(R = 0.42,p = 2.40E-03)。Th1/Th2比值与血清Cys-C相关性良好(R = 0.29,p = 3.10E-02)。
AChR-Ab阳性gMG患者的血清Cys-C水平显著升高,且与疾病严重程度和Th1/Th2比值相关,表明其有可能作为预测MG临床严重程度的有效生物标志物。预计未来大规模样本的前瞻性队列研究将验证这些发现。