Giacalone P L, Boulot P, Deschamps F, Nagy P, Hedon B, Laffargue F, Viala J L
Department of Obstetrics and Gynecology, Hôpital Arnaud de Villeneuve, Montpellier, France.
Prenat Diagn. 1993 Dec;13(12):1133-7. doi: 10.1002/pd.1970131208.
Lymphangiomas or cystic hygromas are malformations of the lymphatic vessels and are characterized by single or multiple cysts which have developed within the soft tissues. They occur most commonly in the neck (75 per cent of cases) and are often associated with hydrops or chromosomal abnormalities (Romero et al., 1988). Mediastinal or abdominal locations are rare and represent less than 5 per cent of cases in the literature (Singh et al., 1971). This paper represents the first reported case of prenatal diagnosis of a lymphangioma in the neck, mediastinum, and abdomen. Diagnosis was made before fetal viability, and allowed us to recommend termination of the pregnancy because of the poor prognosis.
淋巴管瘤或囊状水瘤是淋巴管的畸形,其特征是在软组织内形成单个或多个囊肿。它们最常发生在颈部(75%的病例),并且常与水肿或染色体异常有关(罗梅罗等人,1988年)。纵隔或腹部的病例罕见,在文献中占比不到5%(辛格等人,1971年)。本文报道了首例产前诊断颈部、纵隔和腹部淋巴管瘤的病例。在胎儿具有生存能力之前就做出了诊断,鉴于预后不良,我们建议终止妊娠。