Shauly Y, Weissman A, Meyer E
Department of Ophthalmology, Rambam Medical Center, Haifa, Israel.
J Pediatr Ophthalmol Strabismus. 1993 May-Jun;30(3):178-83. doi: 10.3928/0191-3913-19930501-12.
The clinical features of 63 patients with Duane syndrome are described in this report. All data in the study were gathered retrospectively except for measurements of vertical palpebral fissure and axial eye length, which were investigated prospectively. The following new aspects of the syndrome are emphasized: 1) In most cases with heterotropia, the angle of deviation was not large (< or = 25 prism diopters). 2) Visual acuity of 0.66 (20/30) or better was recorded in 94% of the affected eyes. 3) Smaller palpebral fissure (by 1 mm or more) of the affected eye was measured in primary position among 9 of 40 (22%) unilateral cases. 4) The axial length of the affected eye (mean, 22.8 +/- 0.6 mm) was not significantly different from the uninvolved eye. 5) Two cases of heterochromia iridis (3.2%) were found among the Duane syndrome patients. 6) A 4.8% prevalence of high-tone hearing loss was detected, in addition to 4.8% of sensorineural deafness.
本报告描述了63例杜安综合征患者的临床特征。本研究中的所有数据均为回顾性收集，但垂直睑裂测量和眼轴长度测量为前瞻性研究。该综合征的以下新特点值得关注：1）在大多数斜视病例中，偏斜角度不大（≤25棱镜度）。2）94%的患眼视力记录为0.66（20/30）或更好。3）在40例单侧病例中的9例（22%）中，患眼在第一眼位时睑裂较小（相差1毫米或更多）。4）患眼的眼轴长度（平均22.8±0.6毫米）与未受累眼无显著差异。5）在杜安综合征患者中发现2例虹膜异色症（3.2%）。6）除4.8%的感音神经性耳聋外，还检测到4.8%的高音调听力损失患病率。
