Caballero C, Dolbeau D, Tabone E, Bailly C
Département d'Anatomie et de Cytologie Pathologiques, Centre Léon Bérard, Lyon.
Ann Pathol. 1993;13(3):176-9.
Two cases of giant cell fibroblastoma (GCF) are reported. One presented as cervical tumor in a 11 year old child and the second localized in axillar region of 14 year old boy. Histologically both showed a typical distinctive appearance of this entity when focal fusocellular cells arranged in a storiform pattern was also constated in one. The immunohistochemical and ultrastructural study ruled out a vascular origin. The clinical and pathological findings suggest that CGF represent a juvenile form of dermatofibrosarcoma protuberans.
报告了两例巨细胞纤维母细胞瘤(GCF)。一例表现为一名11岁儿童的颈部肿瘤,另一例位于一名14岁男孩的腋窝区域。组织学上,两者均表现出该实体的典型独特外观,其中一例还发现有局灶性梭形细胞呈束状排列。免疫组化和超微结构研究排除了血管起源。临床和病理结果表明,CGF代表隆突性皮肤纤维肉瘤的一种青少年形式。