蜡样脂褐质沉积症（巴滕病）中的储存小体：低分子量成分、异常氨基酸以及由非荧光成分重构荧光小体 - Suppr

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超能文献

Storage bodies in the ceroid-lipofuscinoses (Batten disease): low-molecular-weight components, unusual amino acids and reconstitution of fluorescent bodies from non-fluorescent components.

作者信息

Palmer D N, Bayliss S L, Clifton P A, Grant V J

机构信息

Department of Veterinary Pathology and Public Health, Massey University, Palmerston North, New Zealand.

出版信息

J Inherit Metab Dis. 1993;16(2):292-5. doi: 10.1007/BF00710268.

DOI:10.1007/BF00710268

PMID:8411984

Abstract

摘要

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本文引用的文献

Ceroid lipofuscinosis in sheep. I. Bis(monoacylglycero)phosphate, dolichol, ubiquinone, phospholipids, fatty acids, and fluorescence in liver lipopigment lipids.

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Lysosomal storage of the DCCD reactive proteolipid subunit of mitochondrial ATP synthase in human and ovine ceroid lipofuscinoses.

Adv Exp Med Biol. 1989;266:211-22; discussion 223. doi: 10.1007/978-1-4899-5339-1_15.

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