Tanwar R K, Kumar R, Malik S, Dhir R, Rath G K
Department of Radiation Therapy, Institute Rotary Cancer Hospital, All India Institute of Medical Sciences, New Delhi, India.
Indian J Pathol Microbiol. 1995 Jan;38(1):91-4.
Malignant peripheral nerve sheath tumours of orbit is rare entity. Only sixteen cases are reported in world literature. Bengin schwannomas of the orbit are found in 1.5 to 18 percent of patients with von Recklinghausen's disease (VRD) and form 1 percent of all orbital tumours1. The incidence of malignant transformation in VRD is varies from 5-15 percent of all the cases1.
眼眶恶性外周神经鞘瘤是一种罕见的疾病。世界文献中仅报道了16例。眼眶的良性神经鞘瘤在1.5%至18%的冯·雷克林豪森病(VRD)患者中被发现,占所有眼眶肿瘤的1%。VRD中恶性转化的发生率在所有病例的5%至15%之间。