Charache S
Johns Hopkins University, Baltimore, MD 21209-4519, USA.
Curr Opin Hematol. 1996 Mar;3(2):139-44. doi: 10.1097/00062752-199603020-00006.
Sudden death in military recruits with sickle cell trait appears to be related to hyperthermia and its consequences and can probably be prevented by use of sensible precautions and heightened awareness of the risk. Sickle cell disease can be treated by decreasing the proportion of sickle cells through transfusion; indications and pathophysiology of such transfusions are beginning to become clear. Sickle cell disease can be prevented if erythrocytes can be prevented from sickling. Dilution of hemoglobin S within erythrocytes, by stimulating fetal hemoglobin production, increasing cell water, or inducing iron deficiency, can achieve that goal in some patients, but risks and benefits of such treatment are still incompletely understood.
具有镰状细胞性状的新兵猝死似乎与体温过高及其后果有关,通过采取合理的预防措施和提高对该风险的认识或许可以预防。镰状细胞病可通过输血降低镰状细胞比例来治疗;此类输血的适应症和病理生理学正逐渐明晰。如果能防止红细胞镰变,镰状细胞病是可以预防的。通过刺激胎儿血红蛋白生成、增加细胞内水分或诱发缺铁来稀释红细胞内的血红蛋白S,在某些患者中可以实现这一目标,但此类治疗的风险和益处仍未完全明了。