Guinamard R, Aspenström P, Fougereau M, Chavrier P, Guillemot J C
Centre d'Immunologie INSERM-CNRS de Marseille-Luminy, Marseille, France.
FEBS Lett. 1998 Sep 4;434(3):431-6. doi: 10.1016/s0014-5793(98)01016-3.
The Wiskott-Aldrich syndrome (WAS) is a rare immunodeficiency disease affecting mainly platelets and lymphocytes. Here, we show that the WAS gene product, WASp, is tyrosine phosphorylated upon aggregation of the high affinity IgE receptor (Fc epsilonRI) at the surface of RBL-2H3 rat tumor mast cells. Lyn and the Bruton's tyrosine kinase (Btk), two protein tyrosine kinases involved in Fc epsilonRI-signaling phosphorylate WASp and interact with WASp in vivo. Interestingly, expression of a GTPase defective mutant form of CDC42, that interacts with WASp, is accompanied by a substantial increase in WASp tyrosine phosphorylation. This study suggests that activated CDC42 recruits WASp to the plasma membrane where it becomes phosphorylated by Lyn and Btk. We conclude that WASp represents a connection between protein tyrosine kinase signaling pathways and CDC42 function in cytoskeleton and cell growth regulation in hematopoietic cells.
威斯科特-奥尔德里奇综合征(WAS)是一种主要影响血小板和淋巴细胞的罕见免疫缺陷疾病。在此,我们发现,在RBL-2H3大鼠肿瘤肥大细胞表面,高亲和力IgE受体(FcεRI)聚集时,WAS基因产物WASp会发生酪氨酸磷酸化。Lyn和布鲁顿酪氨酸激酶(Btk)这两种参与FcεRI信号传导的蛋白酪氨酸激酶在体内使WASp磷酸化并与WASp相互作用。有趣的是,与WASp相互作用的CDC42的GTPase缺陷突变体形式的表达,伴随着WASp酪氨酸磷酸化的显著增加。这项研究表明,活化的CDC42将WASp招募到质膜,在那里它被Lyn和Btk磷酸化。我们得出结论,WASp代表了蛋白酪氨酸激酶信号通路与CDC42在造血细胞的细胞骨架和细胞生长调节中的功能之间的联系。