[遗传性长QT综合征：我们自己的经验]

[Hereditary long QT syndrome: our own experience].

作者信息

Majewski J, Lelakowski J

机构信息

Kliniki Elektrokardiologii Instytutu Kardiologii Collegium Medicum Uniwersytetu Jagiellońskiego w Krakowie.

出版信息

Wiad Lek. 1999;52(1-2):67-73.

PMID:10335128

Abstract

We report the case of 16-year old girl who was admitted to our Department after the episode of ventricular fibrillation. We diagnosed the hereditary long QT syndrome. The patient's family was investigated and complex therapy was started in affected individuals including cardioselective beta-blocker (atenolol) and permanent cardiac pacing (VVIR and DDDR). This therapy is effective in prevention of life-threatening cardiac arrhythmias in our patients.

摘要

我们报告了一名16岁女孩的病例，她在发生室颤后被收治入我们科室。我们诊断其患有遗传性长QT综合征。对患者家族进行了调查，并对受影响个体开始了综合治疗，包括使用心脏选择性β受体阻滞剂（阿替洛尔）和永久性心脏起搏（VVIR和DDDR）。这种治疗对预防我们患者的危及生命的心律失常有效。