Roach E S, DiMario F J, Kandt R S, Northrup H
Division of Child Neurology, University of Texas Southwestern Medical Center at Dallas 75235, USA.
J Child Neurol. 1999 Jun;14(6):401-7. doi: 10.1177/088307389901400610.
At the recent Tuberous Sclerosis Consensus Conference, a subcommittee proposed recommendations to guide the rational use of diagnostic studies in patients with tuberous sclerosis complex. Recommendations were made for diagnostic evaluation at the time of diagnosis, when testing helps both to establish the diagnosis and to identify potential complications. Additional guidelines were proposed for the ongoing surveillance of established patients to detect later complications of tuberous sclerosis complex. In the absence of comprehensive population studies to govern the use of diagnostic studies in individuals with tuberous sclerosis complex, the panel developed guidelines based on the disorder's natural history, concentrating on complications that are common, clinically significant, and more easily managed when found early. Finally, the group made suggestions for the use of diagnostic tests to identify family members who have tuberous sclerosis complex. Although these recommendations should standardize and improve our use of diagnostic studies in individuals with tuberous sclerosis complex, the clinical approach in a given patient must remain flexible enough to meet the needs of individual patients and families.
在最近的结节性硬化症共识会议上,一个小组委员会提出了相关建议,以指导结节性硬化症复合体患者诊断性检查的合理使用。针对诊断时的诊断评估提出了建议,此时进行检测有助于确立诊断并识别潜在并发症。还针对确诊患者的持续监测提出了额外指南,以检测结节性硬化症复合体的后期并发症。由于缺乏全面的人群研究来规范结节性硬化症复合体患者诊断性检查的使用,该小组根据该疾病的自然病程制定了指南,重点关注常见、具有临床意义且早期发现时更易于处理的并发症。最后,该小组就使用诊断测试来识别患有结节性硬化症复合体的家庭成员提出了建议。尽管这些建议应使我们对结节性硬化症复合体患者诊断性检查的使用标准化并加以改进,但针对特定患者的临床方法必须保持足够的灵活性,以满足个体患者及其家庭的需求。