Wong M L, Sim E K, Goh J J, Quek S C, Wong J C, Yip W C, Lee C N
Department of Paediatrics, National University Hospital, Singapore.
Ann Acad Med Singap. 1999 Mar;28(2):237-40.
The Fontan operation has been used to palliate patients with a functional single ventricle. In many such patients the operative risk for a Fontan procedure is high. The bidirectional cavopulmonary anastomosis (BCPA) is a useful intermediate palliative procedure before Fontan correction. It may reduce the deleterious sequelae of chronic hypoxaemia and long-term ventricular overload, thus yielding a more suitable Fontan candidate. We reviewed our experience of 9 patients with univentricular hearts who were at the time of the BCPA not considered suitable candidates for conventional Fontan operation. Two patients had double inlet right ventricle (DIRV) with pulmonary stenosis (PS) and ventricular septal defect (VSD), 2 had univentricular heart, 4 had tricuspid atresia (TA) and hypoplastic right ventricle (RV), 1 patient had atrioventricular septal defect (AVSD) with double outlet right ventricle (DORV) with hypoplastic RV. Two of the 9 patients had bilateral superior vena cavae. All except one had undergone prior palliative operations. The mean age at BCPA was 4.7 years (range 1.5 years to 6 years) and the mean weight at surgery was 15 kg (range 7 to 22 kg). There were no operative deaths. The mean hospitalization stay was 8.5 days (range 5 to 13 days) with a mean follow up of 14 months. Median oxygen saturation improved from 78.7 +/- 6.3% to 85.9 +/- 3.9%. The BCPA is a useful palliative procedure to stage Fontan type reconstruction in selected patients with univentricular hearts.
Fontan手术已被用于缓解功能性单心室患者的症状。在许多此类患者中,Fontan手术的手术风险很高。双向腔肺吻合术(BCPA)是Fontan矫正术前一种有用的中间姑息性手术。它可能会减少慢性低氧血症和长期心室超负荷的有害后遗症,从而产生更适合进行Fontan手术的候选者。我们回顾了9例单心室心脏患者的经验,这些患者在进行BCPA时被认为不适合进行传统的Fontan手术。2例为右心室双入口(DIRV)合并肺动脉狭窄(PS)和室间隔缺损(VSD),2例为单心室心脏,4例为三尖瓣闭锁(TA)合并右心室发育不良(RV),1例为房室间隔缺损(AVSD)合并右心室双出口(DORV)及右心室发育不良。9例患者中有2例有双侧上腔静脉。除1例患者外,所有患者均曾接受过姑息性手术。BCPA时的平均年龄为4.7岁(范围为1.5岁至6岁),手术时的平均体重为15 kg(范围为7至22 kg)。无手术死亡病例。平均住院时间为8.5天(范围为5至13天),平均随访14个月。中位血氧饱和度从78.7±6.3%提高到85.9±3.9%。BCPA是一种有用的姑息性手术,可用于对选定的单心室心脏患者进行Fontan型重建分期。