[Labyrinth involvement in Langerhan's cell histiocytosis].

Langerhans' cell histiocytosis is a rare pathology that implies an abnormal proliferation of these kind of cells associated with granular infiltration that affects different structures of the human body, including the temporal bone. The middle ear and the mastoid are mostly involved (61%). The inner ear is more resistant to the destruction caused by the granulation tissue, but when occurs, an irreversible neurosensorial hearing loss appears. The early diagnose and the choice of the therapeutical sequences are essential to avoid these lesions.