Magnus K G, Millar A J, Sinclair-Smith C C, Rode H
Department of Pediatric Radiology, Institute of Child Health, Red Cross Children's Hospital, Cape Town, South Africa.
J Pediatr Surg. 1999 Dec;34(12):1861-4. doi: 10.1016/s0022-3468(99)90333-0.
The authors report the third case since 1964 of fetus-in-fetu presenting at Red Cross Children's Hospital. A fetal liver abnormality was detected during routine antenatal ultrasound scan, and the postnatal diagnosis of an intrahepatic, multiple fetus-in-fetu was made with abdominal ultrasound scan, plain radiograph of the abdomen and computed tomography. The mass was removed surgically by hemihepatectomy when the patient was 4 months of age. Imaging and the macroscopic and microscopic appearances of the abnormality confirmed the diagnosis and amplified it to include an adjacent teratoma. Multiple small subcapsular and perimass vascular hamartomas were coincidentally discovered in the liver. Two of the 3 nodules within the amniotic-lined cavity of the intrahepatic mass individually comply with the accepted criteria for fetus-in-fetu, and the third nodule has the accepted features of a benign teratoma. The existence of multiple fetus-in-fetu and fetus-in-fetu combined with a teratoma, is recorded in the medical literature. The imaging as well as the macroscopic and microscopic features are illustrated.
作者报告了自1964年以来在红十字儿童医院出现的第三例胎中胎病例。在常规产前超声扫描期间检测到胎儿肝脏异常,产后通过腹部超声扫描、腹部平片和计算机断层扫描对肝内多发胎中胎做出诊断。患儿4个月大时通过半肝切除术手术切除了肿块。该异常的影像学表现以及大体和显微镜下表现证实了诊断,并进一步明确为合并一个相邻的畸胎瘤。在肝脏中偶然发现了多个小的包膜下和肿块周围血管错构瘤。肝内肿块羊膜内衬腔内的3个结节中有2个分别符合胎中胎的公认标准,第三个结节具有良性畸胎瘤的公认特征。医学文献中记载了多发胎中胎以及胎中胎合并畸胎瘤的情况。文中展示了其影像学表现以及大体和显微镜下特征。