Li L, Dowling J E
Department of Molecular Biology, Harvard University, Cambridge, Massachusetts 02138, USA.
J Neurosci. 2000 Mar 1;20(5):1883-92. doi: 10.1523/JNEUROSCI.20-05-01883.2000.
We describe here a dominant mutation, night blindness b (nbb), which causes an age-related visual system defect in zebrafish. At 4-5 months of age, dark-adapted nbb(+/-) mutants show abnormal visual threshold fluctuations when measured behaviorally. Light sensitizes the animals; thus early dark adaptation of nbb(+/-) fish is normal. After 2 hr of dark adaptation, however, visual thresholds of nbb(+/-) mutants are raised on average 2-3 log units, and rod system function is not detectable. Electroretinograms recorded from nbb(+/-) mutants are normal, but ganglion cell thresholds are raised in prolonged darkness, suggesting an inner retinal defect. The visual defect of nbb(+/-) mutants may be likely caused by an abnormal olfactoretinal centrifugal innervation; in nbb(+/-) mutants, the olfactoretinal centrifugal projection to the retina is disrupted, and the number of retinal dopaminergic interplexiform cells is reduced. A similar visual defect as shown by nbb(+/-) mutants is observed in zebrafish in which the olfactory epithelium and olfactory bulb have been excised. Homozygous nbb fish display an early onset neural degeneration throughout the CNS and die by 7-8 d of age.
我们在此描述一种显性突变,夜盲b(nbb),它在斑马鱼中导致与年龄相关的视觉系统缺陷。在4至5个月大时,行为学测量显示,暗适应的nbb(+/-)突变体表现出异常的视觉阈值波动。光会使动物敏感化;因此,nbb(+/-)鱼的早期暗适应是正常的。然而,在暗适应2小时后,nbb(+/-)突变体的视觉阈值平均提高2至3个对数单位,并且无法检测到视杆系统功能。从nbb(+/-)突变体记录的视网膜电图是正常的,但在长时间黑暗中神经节细胞阈值升高,表明视网膜内层存在缺陷。nbb(+/-)突变体的视觉缺陷可能是由嗅觉视网膜离心神经支配异常引起的;在nbb(+/-)突变体中,嗅觉视网膜向视网膜的离心投射被破坏,视网膜多巴胺能双极细胞数量减少。在切除了嗅觉上皮和嗅球的斑马鱼中观察到与nbb(+/-)突变体类似的视觉缺陷。纯合nbb鱼在整个中枢神经系统中表现出早期神经变性,并在7至8日龄时死亡。