Pentimone F, Riccioni S, Del Corso L
Department of Internal Medicine, University of Pisa, Italy.
Panminerva Med. 1999 Dec;41(4):351-4.
A case of Congenital Hypopituitarism (CH) in an untreated 48 yr-old-man is reported. The hormonal studies demonstrated a panhypopituitarism and MR imaging revealed absence of pituitary stalk, small anterior pituitary remnant on the sella floor and ectopic neurohypophysis at the tuber cinereum. The pattern of hormonal responsiveness suggests that CH encompasses findings typical of primary anterior pituitary disease and those of hypothalamic dysfunction.
报告了一例48岁未经治疗的先天性垂体功能减退(CH)男性病例。激素研究显示全垂体功能减退,磁共振成像显示垂体柄缺如、蝶鞍底部有小的垂体前叶残余以及灰结节处有异位神经垂体。激素反应模式表明,先天性垂体功能减退包括原发性垂体前叶疾病和下丘脑功能障碍的典型表现。