De José María B, Drudis R, Monclús E, Silva A, Santander S, Cusí V
Department of Paediatric Anaesthesia Universitat de Barcelona, Barcelona, Spain.
Paediatr Anaesth. 2000;10(4):441-4. doi: 10.1046/j.1460-9592.2000.00549.x.
Complete tracheal agenesis is a very rare congenital anomaly that is only compatible with life in some cases with associated tracheo-oesophageal or broncho-oesophageal fistula. In most cases, concomitant congenital anomalies of the heart, digestive tract or genitourinary tract are present. It should be suspected in any neonate with a history of hydramnios, absent crying, respiratory distress and difficulty in intubation. The possibility for surgical correction or palliation rests on the extent of atresia present. We present a case of complete tracheal agenesis without tracheo nor broncho-oesophageal fistula (type II by Floyd's classification) - the diagnosis of which was prenatally suspected - and discuss the important features of the airway management of this condition.
完全性气管闭锁是一种非常罕见的先天性畸形,仅在某些伴有气管食管或支气管食管瘘的情况下才能存活。大多数情况下,还伴有心脏、消化道或泌尿生殖道的先天性畸形。任何有羊水过多、不哭、呼吸窘迫和插管困难病史的新生儿都应怀疑此病。手术矫正或姑息治疗的可能性取决于闭锁的程度。我们报告一例无气管食管或支气管食管瘘的完全性气管闭锁病例(根据弗洛伊德分类为II型)——产前怀疑此病——并讨论这种情况气道管理的重要特征。