Sandmann W, Schulte K M
Clinic for Vascular Surgery, University Clinics, Heinrich-Heine-University, Düsseldorf, Germany.
Ann Vasc Surg. 2000 Sep;14(5):496-502. doi: 10.1007/s100169910095.
We report here a 9-year-old girl with fibromuscular dysplasia of many muscular arteries including both renal and internal carotid arteries, the celiac artery, superior mesenteric artery, and one external carotid artery. She suffered from severe renovascular hypertension with beginning secondary cardiac decompensation, typical angina abdominalis, and neurological signs, including severe headaches and hemianopsia. Surgery was performed for all major vessels and the outcome is good 2.5 years after the operation. The clinical presentation, differential diagnosis, and treatment options of fibromuscular dysplasia in childhood are discussed and the literature is reviewed.
我们在此报告一名9岁女孩,患有多支肌性动脉的纤维肌发育不良,累及肾动脉、颈内动脉、腹腔干动脉、肠系膜上动脉以及一支颈外动脉。她患有严重的肾血管性高血压,并已开始出现继发性心脏代偿失调、典型的腹型心绞痛以及包括严重头痛和偏盲在内的神经症状。对所有主要血管均进行了手术,术后2.5年效果良好。本文讨论了儿童期纤维肌发育不良的临床表现、鉴别诊断及治疗选择,并对相关文献进行了综述。