Abril J C, Ferrer A, Castillo F, Ferrer-Torrelles M
Pediatric Orthopaedic Department, Hospital del Niño Jesús, Madrid, Spain.
J Pediatr Orthop. 2000 Nov-Dec;20(6):729-35. doi: 10.1097/00004694-200011000-00006.
Radiographic findings in Legg-Calvé-Perthes disease (LCPD) are well known. Four classic stages have been described: incipient stage, avascular stage, fragmentation stage, and residual stage. Final femoral morphology is normally coxa magna, which is associated frequently with hypertrophy of the articular cartilage. We describe five patients with a hip process that initially presented clinical and radiographic findings compatible with LCPD. However, none of these patients showed the typical sequence of the radiographic stages. Instead, the early signs were the formation of rounded areas of rarefaction in the epiphysis and/or the metaphysis with considerable surrounding osteoporosis, early narrowing of the articular space, and final coxa breva morphology with signs of osteoarthritis. No condensation or fragmentation stages were observed. The pathologic study showed complete atrophy of the synovial villi with hyaline cartilage and bone necrosis. The patients described herein presented an intraarticular hip process, initially with signs and symptoms similar to LCPD but with an ultimate clinical evolution that differs from ordinary LCPD.
Legg-Calvé-Perthes病(LCPD)的影像学表现已为人熟知。该病已被描述为四个经典阶段:初期、缺血期、碎裂期和残留期。最终的股骨形态通常为髋外翻,常伴有关节软骨肥大。我们描述了5例髋关节病变患者,其最初的临床和影像学表现与LCPD相符。然而,这些患者均未表现出典型的影像学分期序列。相反,早期征象为骨骺和/或干骺端出现圆形透亮区,周围伴有明显骨质疏松,关节间隙早期变窄,最终形成髋内翻形态并伴有骨关节炎征象。未观察到硬化或碎裂期。病理研究显示滑膜绒毛完全萎缩,伴有透明软骨和骨坏死。本文所述患者表现为关节内髋关节病变,最初的症状和体征与LCPD相似,但最终的临床演变与普通LCPD不同。