Madrigal Rubiales B, Vara A, Ablanedo P, Herreros M, Vazquez L, Fresno M
Servicio de Anatomía Patológica, Hospital Na Sa de Covadonga (HCA), Oviedo, Asturias, España.
Arch Esp Urol. 2001 Mar;54(2):176-80.
A case of idiopathic retroperitoneal fibrosis in a 34-year-old man with anemia and elevated erythrocyte sedimentation rate is presented.
METHODS/RESULTS: Ultrasound, CT and MRI evaluation and pathological study were performed. These diagnostic imaging techniques demonstrated an infiltrating mass in the upper portion of the abdomen which was resected. Histological and immunohistochemical studies of the surgical specimen demonstrated sclerosing retroperitonitis.
Idiopathic retroperitoneal fibrosis (Ormond's disease) is a rare disease entity whose etiology is obscure and is characterized by retroperitoneal fibrosis with inflammatory infiltrates composed of plasma cells, lymphocytes and eosinophils. This case is of interest due to its atypical location, and because the patient was young with no remarkable clinical history and only mild anemia and an elevated erythrocyte sedimentation rate.
报告一例34岁男性特发性腹膜后纤维化病例,该患者伴有贫血且红细胞沉降率升高。
方法/结果:进行了超声、CT和MRI评估及病理研究。这些诊断成像技术显示上腹部有一浸润性肿块,该肿块已被切除。手术标本的组织学和免疫组化研究显示为硬化性腹膜炎。
特发性腹膜后纤维化(奥蒙德病)是一种罕见的疾病实体,其病因不明,特征为腹膜后纤维化伴浆细胞、淋巴细胞和嗜酸性粒细胞组成的炎性浸润。该病例因其非典型位置而备受关注,且患者年轻,无明显临床病史,仅有轻度贫血和红细胞沉降率升高。