Sudre-Levillain I, Roman S, Nicollas R, Triglia J M
Service d'ORL et de chirurgie cervicofaciale pédiatrique, CHU Timone, 264, rue Saint-Pierre, 13385 Marseille, France.
Arch Pediatr. 2001 Jul;8(7):757-62. doi: 10.1016/s0929-693x(00)90313-0.
Tracheomalacia is characterized by an expiratory tracheal collapse. The revealing clinical features usually occur after a symptom-free period during the first year of life (during the first three months in 60% of cases): mainly stridor, wheezing, chronic cough, apnoeic attacks, and difficult breathing. Tracheoscopy allows the differentiation of primary tracheomalacia and tracheomalacia secondary to pressure on the trachea from the vascular ring or mediastinal tumour. Tracheomalacia is also frequently associated with oesophageal atresia. Surgical treatment is indicated in severe and secondary forms.
气管软化症的特征是呼气时气管塌陷。典型的临床特征通常在出生后第一年无症状期后出现(60%的病例在头三个月):主要为喘鸣、喘息、慢性咳嗽、呼吸暂停发作和呼吸困难。气管镜检查可区分原发性气管软化症和继发于血管环或纵隔肿瘤对气管压迫的气管软化症。气管软化症也常与食管闭锁相关。严重和继发性形式的气管软化症需要手术治疗。