儿童虹膜新生血管作为潜在髓上皮瘤的一种表现。
Iris neovascularization in children as a manifestation of underlying medulloepithelioma.
作者信息
Singh A, Singh A D, Shields C L, Shields J A
机构信息
Scheie Eye Institute, University of Pennsylvania, USA.
出版信息
J Pediatr Ophthalmol Strabismus. 2001 Jul-Aug;38(4):224-8. doi: 10.3928/0191-3913-20010701-09.
PURPOSE
To report the occurrence of unilateral iris neovascularization in children secondary to medulloepithelioma.
METHODS
Presenting features and the clinical course of patients confirmed to have medulloepithelioma were reviewed.
RESULTS
Seven patients with medulloepithelioma had iris neovascularization during the clinical course. Associated cataract and lens coloboma occurred in two and three cases, respectively. In six (86%) cases, no apparent cause for iris neovascularization could be detected at presentation. Two cases had tube shunts for management of neovascular glaucoma before medulloepithelioma was recognized. All cases eventually required enucleation.
CONCLUSION
Presence of iris neovascularization is an early manifestation of medulloepithelioma. Children with iris neovascularization of unknown cause should be evaluated to exclude underlying medulloepithelioma.
目的
报告儿童髓上皮瘤继发单侧虹膜新生血管形成的病例。
方法
回顾确诊为髓上皮瘤患者的临床表现及临床病程。
结果
7例髓上皮瘤患者在临床病程中出现虹膜新生血管形成。分别有2例和3例伴有白内障和晶状体缺损。6例（86%）患者在初诊时未发现虹膜新生血管形成的明显病因。2例在髓上皮瘤被确诊之前因新生血管性青光眼接受了引流管植入术。所有病例最终均需行眼球摘除术。
结论
虹膜新生血管形成是髓上皮瘤的早期表现。对于不明原因的虹膜新生血管形成的儿童，应进行评估以排除潜在的髓上皮瘤。
Zotero 插件