Sharma M C, Arora R, Sharma P, Mehta V S, Sarkar C
Department of Neuropathology, All India Institute of Medicial Sciences, New Delhi 110029, India.
Childs Nerv Syst. 2001 Nov;17(11):689-92. doi: 10.1007/s003810100448. Epub 2001 Aug 28.
Presence of heterotopic dysplastic renal tissue in the lumbosacral region is an extremely uncommon condition.
We report the first case of diastematomyelia associated with ectopic renal tissue. A 10-month-old male child presented with lipomeningomyelocele associated with spina bifida in the lumbosacral region, and the lipoma was excised. Imaging of the spine at 5 years of age showed spina bifida, bony diastematomyelia, lipomeningomyelocele and a small intraspinal cystic lesion. The boy was then operated upon at the age of 5 years, and histopathological examination of the cystic lesion revealed ectopic dysplastic renal tissue.
腰骶部存在异位发育异常的肾组织是一种极其罕见的情况。
我们报告首例与异位肾组织相关的脊髓纵裂病例。一名10个月大的男童因腰骶部脊柱裂合并脂肪脊髓脊膜膨出就诊,随后切除了脂肪瘤。5岁时的脊柱影像学检查显示脊柱裂、骨性脊髓纵裂、脂肪脊髓脊膜膨出和一个小的脊髓内囊性病变。该男孩随后在5岁时接受了手术,对囊性病变的组织病理学检查显示为异位发育异常的肾组织。