Maresi E, Passantino R, Midulla R, Ottoveggio G, Orlando E, Becchina G, Meschis L, Amato G
Department of Pathology, University of Palermo, Palermo, Italy.
Hum Pathol. 2001 Dec;32(12):1407-9. doi: 10.1053/hupa.2001.29683.
This article describe's a case of atypical Kawasaki disease (AKD) with lack of typical clinical signs and rapid fatal course in a 2-month-old infant, who 1 week before hospitalization demonstrated rhinitis, coughing without fever, and later conjunctival hyperemia and allergic exanthema on chest and arms. On admittance, labwork highlighted the following: leukocytosis, thrombocytosis, elevated sedimentation rate, and positive C-reactive protein. General conditions remained mediocre for 7 days until sudden death occurred. The autopsy confirmed death caused by cardiac tamponade caused by a ruptured inflammated aneurysm of the left anterior descending coronary artery. We believe that the currently accepted clinical diagnostics criteria for KD in infants 2 years of age or younger can cause missed in vita diagnosis of AKD. For such, any typical clinical sign of KD whenever associated with thrombocytosis and elevated indices of phlogosis, should led to suspicion of KD and permit cardiovascular examination, and thus early treatment.
本文描述了一例2个月大婴儿患非典型川崎病(AKD)的病例,该患儿缺乏典型临床症状且病程进展迅速并致命。住院前1周,患儿出现鼻炎、无发热咳嗽,随后出现结膜充血以及胸部和手臂的过敏性皮疹。入院时,实验室检查结果显示:白细胞增多、血小板增多、血沉升高以及C反应蛋白呈阳性。患儿一般状况在7天内一直欠佳,直至突然死亡。尸检证实死亡原因是左前降支冠状动脉炎性动脉瘤破裂导致的心包填塞。我们认为,目前被广泛接受的2岁及以下婴儿川崎病临床诊断标准可能导致AKD的生前漏诊。因此,只要出现任何川崎病的典型临床症状并伴有血小板增多和炎症指标升高,就应怀疑川崎病,并进行心血管检查,从而实现早期治疗。