Villegas García M, Espinosa García M D, Ramos Martín J L, Soria Arcos F, de la Morena Valenzuela G, Valdés Chavarri M
Servicio de Cardiología, Hospital Universitario Virgen de la Arrixaca, 30120, Murcia, Spain.
Eur J Echocardiogr. 2001 Sep;2(3):205-6. doi: 10.1053/euje.2001.0090.
Congenital right ventricular muscular diverticula are extremely rare and are usually associated with other congenital cardiac anomalies, (in half of the cases tetralogy of Fallot). They functionally behave like an accessory ventricular chamber which contracts synchronously with the normal ventricles. Less than 30 patients with a right ventricular diverticulum have been reported in literature. An apical right ventricular diverticulum occurs in patients with thoraco-abdominal midline defects or abnormalities of the cardiac position([1]). However, an antero-superior diverticulum is usually associated with other congenital cardiac defects, such as a ventricular septal defect, tetralogy of Fallot, double outlet right ventricle and pulmonary stenosis([2--9]). We report an 11-year-old boy with an antero-superior diverticulum of the right ventricle associated with a coarctation of aorta, ductus arteriosus, and atrial and ventricular septum defects. To the best of our knowledge, such an association has not been reported before.
先天性右心室肌性憩室极为罕见,通常与其他先天性心脏异常相关(半数病例为法洛四联症)。其功能上表现为一个与正常心室同步收缩的附属心室腔。文献报道的右心室憩室患者不足30例。心尖部右心室憩室见于胸腹中线缺损或心脏位置异常的患者([1])。然而,前上型憩室通常与其他先天性心脏缺陷相关,如室间隔缺损、法洛四联症、右心室双出口和肺动脉狭窄([2 - 9])。我们报告一名11岁男孩,其右心室前上型憩室合并主动脉缩窄、动脉导管未闭以及房间隔和室间隔缺损。据我们所知,此前尚未有此类关联的报道。