Cochlear implantation in a patient with superficial siderosis of the central nervous system.

OBJECTIVE

To perform an assessment of the viability of cochlear implantation in a patient with superficial siderosis of the brain.

STUDY DESIGN

Case review.

SETTING

Tertiary referral center.

PATIENTS

Patient with superficial siderosis of the brain.

INTERVENTION

Cochlear implantation.

MAIN OUTCOME MEASURES

Electrically evoked auditory brainstem responses and fitting strategy for cochlear implant based on patient's subjective responses.

RESULTS

After some time, C levels and T levels showed a pattern comparable with the evoked auditory brainstem responses.

CONCLUSIONS

Bilateral profound hearing loss after superficial siderosis of the brain is no absolute contraindication for implantation. Furthermore, evoked auditory brainstem measurements can potentially guide the fitting process of the implant in difficult cases.