Shundo Y, Ota S, Inaba H, Eto T, Honda A, Suzuki M, Muro H
Department of Thoracic Surgery, Shizuoka General Hospital, Fujieda, Japan.
Kyobu Geka. 2002 Sep;55(10):847-51.
Angiosarcomas rarely develop within a peripheral nerve or a peripheral nerve sheath tumor. A 68-year-old woman was admitted for right hemothorax. She had suffered from the left thoracic empyema and the right chest wall tumor which had been regarded as schwannoma clinically. Anemia got serious due to continuous bloody effusion. Although bleeding point was not detected by thoracotomy. The right chest wall tumor was resected. Postoperatively bloody effusion still drained continuously, she died ten days after the operation. Resected tumor was almost necrotized. The tumor was diagnosed as angiosarcoma pathologically, in which a part of schwannoma component resided. It is indicated that angiosarcoma in this case arised from degenerated schwannoma. It is necessary to consider angiosarcoma, rarely arised from degenerated schwannoma, during conservative, long-term observation on the care of schwannoma.
血管肉瘤很少发生于周围神经或周围神经鞘瘤内。一名68岁女性因右侧血胸入院。她曾患左侧胸腔积脓和右侧胸壁肿瘤,临床上曾被视为神经鞘瘤。由于持续的血性胸腔积液,贫血加重。尽管开胸手术未发现出血点,但仍切除了右侧胸壁肿瘤。术后血性胸腔积液仍持续引流,患者术后十天死亡。切除的肿瘤几乎坏死。病理诊断为血管肉瘤,其中存在部分神经鞘瘤成分。提示该病例中的血管肉瘤起源于退变的神经鞘瘤。在对神经鞘瘤进行保守、长期观察时,有必要考虑血管肉瘤,尽管其很少起源于退变的神经鞘瘤。