非致密型心肌病的无创和有创评估

Noninvasive and invasive evaluation of noncompaction cardiomyopathy.

作者信息

Bax Jeroen J, Atsma Douwe E, Lamb Hildo J, Rebergen Sidney A, Bootsma Marianne, Voogd Paul J, Somer Soeresh, Schalij Martin J, de Roos Albert, van der Wall Ernst E

出版信息

J Cardiovasc Magn Reson. 2002;4(3):353-7. doi: 10.1081/jcmr-120013302.

DOI:10.1081/jcmr-120013302

PMID:12234106

Abstract

Noncompaction cardiomyopathy is a recently described rare congenital cardiomyopathy; patients can be asymptomatic or develop diastolic and/or systolic left ventricular dysfunction with heart failure, systemic emboli or ventricular arrhythmias. Long-term prognosis is poor. Currently, diagnosis is based on findings on 2D echocardiography; in the current case report we demonstrate the use of MRI to diagnose noncompaction cardiomyopathy.

摘要

致密化不全型心肌病是一种最近才被描述的罕见先天性心肌病；患者可能无症状，或出现舒张期和/或收缩期左心室功能障碍，并伴有心力衰竭、全身性栓塞或室性心律失常。长期预后较差。目前，诊断基于二维超声心动图的检查结果；在本病例报告中，我们展示了使用磁共振成像来诊断致密化不全型心肌病。