Müller J, Kiechl S, Wenning G K, Seppi K, Willeit J, Gasperi A, Wissel J, Gasser T, Poewe W
University Hospital of Neurology, Innsbruck, Austria.
Neurology. 2002 Sep 24;59(6):941-3. doi: 10.1212/01.wnl.0000026474.12594.0d.
The prevalence of primary dystonia was assessed in a random population sample of individuals aged 50 and over in Bruneck, South Tyrol. The diagnosis of primary dystonia was confirmed by videotaped review. Primary dystonia was present in 6 of 707 cases resulting in a prevalence rate of 732 per 100,000 (95% CI 319-1,564) in the general population aged 50 and over. Only two cases (33%) had been previously diagnosed. These results indicate that the true prevalence of primary dystonia is significantly higher than published rates.
在南蒂罗尔州布鲁内克对50岁及以上的随机人群样本进行原发性肌张力障碍患病率评估。原发性肌张力障碍的诊断通过录像回顾得到确认。707例中有6例确诊为原发性肌张力障碍,在50岁及以上的普通人群中患病率为每10万732例(95%可信区间319 - 1564)。此前仅两例(33%)被诊断过。这些结果表明原发性肌张力障碍的实际患病率显著高于已公布的患病率。