Albayram Sait, Kizilkilic Osman, Zulfikar Zuzan, Islak Civan, Kocer Naci
Department of Radiology, Division of Neuroradiology, The Cerrahpasa Medical School, 34300 Kocamustafapasa, Istanbul, Turkey.
Neuroradiology. 2002 Dec;44(12):1004-7. doi: 10.1007/s00234-002-0853-4. Epub 2002 Oct 3.
There are very few reported cases of Erdheim-Chester disease that document involvement of dura at the level of the spinal cord. Among these reports, we know of no publication that includes detailed MRI findings. To the best of our knowledge, the case presented here is the first published report of this specific manifestation of Erdheim-Chester disease that includes detailed MRI findings in addition to the related history. Spinal manifestations of Erdheim-Chester disease in our patient were at the dorsal and lumbar levels (T1-T6 and T12-T11 respectively). Both epidural and subdural linear large masses were present, causing spinal cord compression at the dorsal level and epidural thickening at the lumbar level.
报道的埃尔德海姆-切斯特病累及脊髓硬膜的病例非常少。在这些报道中,我们未发现有包含详细MRI表现的出版物。据我们所知,此处呈现的病例是埃尔德海姆-切斯特病这一特定表现的首次发表报道,除了相关病史外,还包括详细的MRI表现。我们患者的埃尔德海姆-切斯特病脊髓表现位于胸段和腰段(分别为T1-T6和T12-L1)。硬膜外和硬膜下均有线性大肿块,导致胸段脊髓受压和腰段硬膜外增厚。