马蹄肾一侧出现多囊性发育不良，伴有巨输尿管和下段输尿管闭锁。

Multicystic dysplasia in one-half of a horseshoe kidney with megaureter and lower ureteric atresia.

作者信息

Sripathi V

机构信息

Department of Pediatric Urology, CHILDS Trust Hospital, Sundaram Medical Foundation Community Hospital, Chennai, South India.

出版信息

Pediatr Surg Int. 2002 Dec;18(8):735-6. doi: 10.1007/s00383-002-0789-0. Epub 2002 Nov 12.

DOI:10.1007/s00383-002-0789-0

PMID:12598977

Abstract

During evaluation of chronic abdominal pain, a 9-year-old male was found to have a horseshoe kidney (HSK) with multicystic dysplasia (MCD) of the left-sided component. Attached to the MCD was a very large, tortuous ureter occupying almost the whole left side of the abdomen. This ureter on dissection was found to end blindly adjacent to the bladder. MCD of one-half of a HSK is an unusual lesion. Its association with a large megaureter with juxtavesical atresia is a unique event. In HSKs, controversy exists about the need to remove a small dysplastic segment. If this segment is associated with a large ureter, as in our case, removal is mandatory in order to avoid pain and infection.

摘要

在对一名慢性腹痛的9岁男性进行评估时，发现其患有马蹄肾（HSK），左侧部分伴有多囊性发育不良（MCD）。附着在MCD上的是一条非常粗大、迂曲的输尿管，几乎占据了整个左侧腹部。经解剖发现，这条输尿管在膀胱附近呈盲端终止。马蹄肾一侧的MCD是一种不寻常的病变。它与一条伴有膀胱旁闭锁的巨大输尿管相关联是一个独特的情况。对于马蹄肾，是否需要切除小的发育不良节段存在争议。如果该节段与一条粗大的输尿管相关，如我们的病例，为避免疼痛和感染，切除是必要的。