Karnitis S A, Burns K, Sudduth K W, Golden W L, Wilson W G
Department of Pediatrics, University of Virginia Health Sciences Center, Charlottesville 22908.
Am J Med Genet. 1992 Sep 15;44(2):153-7. doi: 10.1002/ajmg.1320440207.
We report on a 4-year-old girl with distinctive facial features (redundant skin, bushy eyebrows, narrow palpebral fissures, short, upturned nose, epicanthal folds, and a long upper lip with well-defined philtrum) who has an interstitial deletion of chromosome 14 including band 14q31, designated as 46,XX,del(14)(pter-->q24.3::q32.1-->qter). Comparison with previously reported patients with deletions of 14q involving band 14q31 suggests that there is a distinctive clinical phenotype associated with this deletion. Our patient had dental abnormalities (3 maxillary and 3 mandibular incisors) not described in the other patients.
我们报告了一名4岁女孩,其具有独特的面部特征(皮肤冗余、眉毛浓密、睑裂狭窄、短而上翘的鼻子、内眦赘皮以及带有明显人中的长上唇),她存在14号染色体的间质缺失,包括14q31带,核型为46,XX,del(14)(pter→q24.3::q32.1→qter)。与先前报道的涉及14q31带的14q缺失患者相比,提示该缺失存在独特的临床表型。我们的患者有其他患者未描述的牙齿异常(上颌3颗和下颌3颗切牙)。