Goldberg Cory, DeLorie Raylene, Zuker Ronald M, Manktelow Ralph T
Department of Plastic Surgery, University of Toronto, Toronto, Ontario, Canada.
J Craniofac Surg. 2003 Sep;14(5):687-90. doi: 10.1097/00001665-200309000-00015.
Speech and communication are major problems for children with Moebius syndrome, a congenital anomaly that includes facial and abducens nerve paralysis and, often, other cranial nerve deficits. In addition, these children frequently have severe functional problems such as drooling as well as poor self-esteem. The purpose of this study was to investigate the outcome of speech with bilateral gracilis muscle transplants innervated by the masseteric nerve in children with Moebius syndrome. The outcome of this two-stage procedure was investigated in 12 patients. Assessments were done before and after surgery, and additional data were collected from video records. After surgery, the children showed improved intelligibility of speech with a significantly lower frequency of all compensatory phonemes, including the sounds of /p/, /b/, /m/, /w/, "sh", /f/, and /v/. This procedure had evident positive impact in all problematic areas and is the procedure of choice for these unfortunate children.
对于患有莫比乌斯综合征的儿童来说，言语和沟通是主要问题。莫比乌斯综合征是一种先天性异常疾病，包括面部和展神经麻痹，且常常伴有其他颅神经缺陷。此外，这些儿童经常存在严重的功能问题，如流口水以及自尊心低落。本研究的目的是调查在患有莫比乌斯综合征的儿童中，采用咬肌神经支配双侧股薄肌移植术对言语产生的效果。对12例患者进行了这一两阶段手术的效果调查。在手术前后进行了评估，并从视频记录中收集了额外数据。手术后，孩子们的言语清晰度有所提高，包括/p/、/b/、/m/、/w/、“sh”、/f/和/v/等所有代偿性音素的出现频率显著降低。该手术在所有问题领域都产生了明显的积极影响，是这些不幸儿童的首选手术方法。
