Sreetharan S S, Prepageran N, Razak A, Valuyeetham K A
ENT Department, Hospital Universiti Kebangsaan Malaysia, Jalan Tenteram, Cheras, 56000, Kuala Lumpur.
Med J Malaysia. 2003 Jun;58(2):290-3.
Aerodigestive amyloidosis is a rare disorder characterized by fibrillar protein deposition in the aerodigestive tree. We present a case of a 19-year-old Chinese gentleman whose diagnosis was initially missed as he presented with features suggestive of severe bronchial asthma and was intubated and ventilated. He subsequently presented 2 years later with severe stridor and required emergency tracheostomy. Current literature is reviewed for the histopathology, common clinical features, radiological findings and treatment options for aerodigestive amyloidosis.