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继发于未被怀疑的普通可变免疫缺陷的儿童自身免疫性血细胞减少症。

Childhood autoimmune cytopenia secondary to unsuspected common variable immunodeficiency.

作者信息

Heeney Matthew M, Zimmerman Sherri A, Ware Russell E

机构信息

Division of Hematology/Oncology, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina 27710, USA.

出版信息

J Pediatr. 2003 Nov;143(5):662-5. doi: 10.1067/S0022-3476(03)00445-1.

Abstract

Immune thrombocytopenic purpura and autoimmune hemolytic anemia are typically idiopathic processes without underlying systemic illness. Four children with autoimmune cytopenia had low immunoglobulin levels that led to the diagnosis of common variable immunodeficiency. Routine screening of immunoglobulins is suggested for children with chronic or recurrent immune thrombocytopenic purpura and autoimmune hemolytic anemia.

摘要

免疫性血小板减少性紫癜和自身免疫性溶血性贫血通常是特发性疾病,无潜在的全身性疾病。四名患有自身免疫性血细胞减少症的儿童免疫球蛋白水平较低,从而诊断为常见变异型免疫缺陷病。建议对患有慢性或复发性免疫性血小板减少性紫癜和自身免疫性溶血性贫血的儿童进行免疫球蛋白常规筛查。

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